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LMX1AMoebius syndrome

In one unrelated proband ([PMID:36381759]), a heterozygous missense variant, p.Gln61Arg, was identified in LMX1A exon 3 by array comparative genomic hybridization and exome sequencing. The patient exhibited facial paralysis with ocular abduction anomalies, dysphagia (HP:0002015), hypertelorism (HP:0000316), short nose (HP:0003196), and restricted jaw movements. No family segregation data or additional cases have been reported. No functional studies of LMX1A have been performed in Moebius syndrome.

References

  • Cureus • 2022 • A Missense Mutation in LMX1A in a Patient With Moebius Syndrome: A Case Report. PMID:36381759

Evidence Based Scoring (AI generated)

Gene–Disease Association

Limited

Single proband, no segregation or replication

Genetic Evidence

Limited

One heterozygous missense variant in one patient ([PMID:36381759])

Functional Evidence

Limited

No functional data for LMX1A in Moebius syndrome