Variant Synonymizer: Platform to identify mutations defined in different ways is available now!

VarSy

Over 2,000 gene–disease validation summaries are now available—no login required!

Browse Summaries

RAD51 – Familial Congenital Mirror Movements

RAD51 has been proposed as an autosomal dominant contributor to isolated congenital mirror movements (MMs), a rare axonal guidance disorder characterized by involuntary contralateral motor mimicry of intentional movements. One report described a boy with mirror movements and incomitant strabismus consistent with cranial dysinnervation, noting that mutations in RAD51 or DCC can underlie isolated congenital MMs (PMID:25838174). In a separate four-generation Italian family with MMs (HP:0001335), sequencing of RAD51 and DCC in ten affected individuals failed to identify pathogenic variants, and segregation analysis was not informative for RAD51 (PMID:30713853).

Current evidence for RAD51 in familial congenital mirror movements is limited to anecdotal case descriptions without variant-level or segregation confirmation. No functional or experimental studies have assessed RAD51 variant impact in the context of MMs. Additional reports of segregating RAD51 mutations, complemented by in vitro or in vivo modeling, are needed to establish a definitive gene-disease relationship.

References

  • Journal of AAPOS | 2015 | Congenital cranial dysinnervation disorder in a boy with congenital mirror movements. PMID:25838174
  • Movement disorders clinical practice | 2014 | Congenital Mirror Movements in a New Italian Family. PMID:30713853

Evidence Based Scoring (AI generated)

Gene–Disease Association

Limited

Inherited autosomal dominant signal in one proband and one family without identified RAD51 variants; no segregation or variant-level data.

Genetic Evidence

Limited

Only anecdotal mention of RAD51 mutations in isolated cases with mirror movements; no pathogenic variants reported.

Functional Evidence

No evidence

No functional assays or experimental models link RAD51 variants to congenital mirror movements.