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RFX2 – Cerebral palsy

In a cohort of 183 Cerebral palsy cases subjected to whole-exome sequencing, de novo protein-altering variants were identified in 43 of 98 case-parent trios. Among six novel candidate genes, one RFX2 de novo missense variant c.272A>G (p.Tyr91Cys) was detected in a single proband, implicating RFX2 in CP pathogenesis (PMID:25666757). This solitary observation provides limited genetic evidence with no additional segregation or recurrence, and the mechanistic role of RFX2 in motor and posture dysfunction remains uncharacterized.

References

  • Molecular psychiatry • 2015 • Whole-exome sequencing points to considerable genetic heterogeneity of cerebral palsy. PMID:25666757

Evidence Based Scoring (AI generated)

Gene–Disease Association

Limited

Single de novo missense variant in one CP proband with no replication or segregation ([PMID:25666757])

Genetic Evidence

Limited

One de novo protein-altering variant in RFX2 in a case-parent trio without additional affected relatives ([PMID:25666757])

Functional Evidence

Limited

No functional data linking RFX2 variants to cerebral palsy